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Ch. IV
ICD-10
Ch. IV
E71
E71
3-char group
Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
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⇄ Primary-code rule changed vs QĐ4469
Coding rules (TT06)
●
Avoid — more specific 4-5 char codes exist (see below)
Codes within E71
E71.0
Maple-syrup-urine disease
E71.1
Other disorders of branched-chain amino-acid metabolism
E71.2
Disorder of branched-chain amino-acid metabolism, unspecified
E71.3
Disorders of fatty-acid metabolism
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