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Ch. IV
ICD-10
Ch. IV
E71.0
E71.0
Maple-syrup-urine disease
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Sibling codes
E71
Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
E71.1
Other disorders of branched-chain amino-acid metabolism
E71.2
Disorder of branched-chain amino-acid metabolism, unspecified
E71.3
Disorders of fatty-acid metabolism
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