E71.3
Disorders of fatty-acid metabolism
Coding guidance (WHO 2019)
Adrenoleukodystrophy [Addison-Schilder] Muscle carnitine palmityltransferase deficiency Very long chain acyl-CoA dehydrogenase (VLCAD) deficiency Excl.: Schilder disease (G37.0)
Adrenoleukodystrophy [Addison-Schilder] Muscle carnitine palmityltransferase deficiency Very long chain acyl-CoA dehydrogenase (VLCAD) deficiency Excl.: Schilder disease (G37.0)