J99.1** Asterisk (manifestation)
Respiratory disorders in other diffuse connective tissue disorders
Coding rules (TT06)
- ●Cannot be used as primary diagnosis
Dual coding (†/*)
This is an asterisk (*) manifestation code — usually paired with a dagger (†) etiology code.
→ Full dagger (†) ↔ asterisk (*) mapping tableCoding guidance (WHO 2019)
Respiratory disorders in: dermatomyositis (M33.0-M33.1†) granulomatosis with polyangiitis (M31.3†) polymyositis (M33.2†) sicca syndrome [Sjögren] (M35.0†) systemic: lupus erythematosus (M32.1†) sclerosis (M34.8†) Wegener granulomatosis (M31.3†)