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J99.1** Asterisk (manifestation)

Respiratory disorders in other diffuse connective tissue disorders

Coding rules (TT06)

  • Cannot be used as primary diagnosis

Dual coding (†/*)

This is an asterisk (*) manifestation code — usually paired with a dagger (†) etiology code.

→ Full dagger (†) ↔ asterisk (*) mapping table

Coding guidance (WHO 2019)

Respiratory disorders in: dermatomyositis (M33.0-M33.1†) granulomatosis with polyangiitis (M31.3†) polymyositis (M33.2†) sicca syndrome [Sjögren] (M35.0†) systemic: lupus erythematosus (M32.1†) sclerosis (M34.8†) Wegener granulomatosis (M31.3†)

Sibling codes

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