E78.6
Lipoprotein deficiency
Coding guidance (WHO 2019)
Abetalipoproteinaemia High-density lipoprotein deficiency Hypoalphalipoproteinaemia Hypobetalipoproteinaemia (familial) Lecithin cholesterol acyltransferase deficiency Tangier disease
Sibling codes
E78Disorders of lipoprotein metabolism and other lipidaemiasE78.0Pure hypercholesterolaemiaE78.1Pure hyperglyceridaemiaE78.2Mixed hyperlipidaemiaE78.3HyperchylomicronaemiaE78.4Other hyperlipidaemiaE78.5Hyperlipidaemia, unspecifiedE78.8Other disorders of lipoprotein metabolismE78.9Disorder of lipoprotein metabolism, unspecified