E78.0
Pure hypercholesterolaemia
Coding guidance (WHO 2019)
Familial hypercholesterolaemia Fredrickson hyperlipoproteinaemia, type IIa Hyperbetalipoproteinaemia Hyperlipidaemia, group A Low-density-lipoprotein-type [LDL] hyperlipoproteinaemia
Sibling codes
E78Disorders of lipoprotein metabolism and other lipidaemiasE78.1Pure hyperglyceridaemiaE78.2Mixed hyperlipidaemiaE78.3HyperchylomicronaemiaE78.4Other hyperlipidaemiaE78.5Hyperlipidaemia, unspecifiedE78.6Lipoprotein deficiencyE78.8Other disorders of lipoprotein metabolismE78.9Disorder of lipoprotein metabolism, unspecified