E753-char group
Disorders of sphingolipid metabolism and other lipid storage disorders
⇄ Primary-code rule changed vs QĐ4469
Coding rules (TT06)
- ●Avoid — more specific 4-5 char codes exist (see below)
Coding guidance (WHO 2019)
Excl.: mucolipidosis, types I-III (E77.0-E77.1) Refsum disease (G60.1)