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E753-char group

Disorders of sphingolipid metabolism and other lipid storage disorders

Primary-code rule changed vs QĐ4469

Coding rules (TT06)

  • Avoid — more specific 4-5 char codes exist (see below)

Coding guidance (WHO 2019)

Excl.: mucolipidosis, types I-III (E77.0-E77.1) Refsum disease (G60.1)

Codes within E75