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J84.1

Other interstitial pulmonary diseases with fibrosis

Coding guidance (WHO 2019)

Diffuse pulmonary fibrosis Fibrosing alveolitis (cryptogenic) Hamman-Rich syndrome Idiopathic pulmonary fibrosis Usual interstitial pneumonia Excl.: pulmonary fibrosis (chronic): due to inhalation of chemicals, gases, fumes or vapours (J68.4) following radiation (J70.1)

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