F84.2
Rett syndrome
⇄ Primary-code rule changed vs QĐ4469
Coding rules (TT06)
- ●Applies only/mainly to females
Coding guidance (WHO 2019)
A condition, so far found only in girls, in which apparently normal early development is followed by partial or complete loss of speech and of skills in locomotion and use of hands, together with deceleration in head growth, usually with an onset between seven and 24 months of age. Loss of purposive hand movements, hand-wringing stereotypies, and hyperventilation are characteristic. Social and play development are arrested but social interest tends to be maintained. Trunk ataxia and apraxia start to develop by age four years and choreoathetoid movements frequently follow. Severe mental retardation almost invariably results.
Sibling codes
F84Pervasive developmental disordersF84.0Childhood autismF84.1Atypical autismF84.3Other childhood disintegrative disorderF84.4Overactive disorder associated with mental retardation and stereotyped movementsF84.5Asperger syndromeF84.8Other pervasive developmental disordersF84.9Pervasive developmental disorder, unspecified