E80.2
Other porphyria
Coding guidance (WHO 2019)
Hereditary coproporphyria Porphyria: NOS acute intermittent (hepatic) Use additional external cause code (Chapter XX), if desired, to identify cause.
Sibling codes
E80Disorders of porphyrin and bilirubin metabolismE80.0Hereditary erythropoietic porphyriaE80.1Porphyria cutanea tardaE80.3Defects of catalase and peroxidaseE80.4Gilbert syndromeE80.5Crigler-Najjar syndromeE80.6Other disorders of bilirubin metabolismE80.7Disorder of bilirubin metabolism, unspecified