E76.2
Other mucopolysaccharidoses
Coding guidance (WHO 2019)
Beta-glucuronidase deficiency Mucopolysaccharidosis, types III, IV, VI, VII Syndrome: Maroteaux-Lamy (mild)(severe) Morquio(-like)(classic) Sanfilippo (type B)(type C)(type D)
Beta-glucuronidase deficiency Mucopolysaccharidosis, types III, IV, VI, VII Syndrome: Maroteaux-Lamy (mild)(severe) Morquio(-like)(classic) Sanfilippo (type B)(type C)(type D)