E74.1
Disorders of fructose metabolism
Coding guidance (WHO 2019)
Essential fructosuria Fructose-1,6-diphosphatase deficiency Hereditary fructose intolerance
Sibling codes
E74Other disorders of carbohydrate metabolismE74.0Glycogen storage diseaseE74.2Disorders of galactose metabolismE74.3Other disorders of intestinal carbohydrate absorptionE74.4Disorders of pyruvate metabolism and gluconeogenesisE74.8Other specified disorders of carbohydrate metabolismE74.9Disorder of carbohydrate metabolism, unspecified