E72.2
Disorders of urea cycle metabolism
Coding guidance (WHO 2019)
Argininaemia Argininosuccinic aciduria Citrullinaemia Hyperammonaemia Excl.: disorders of ornithine metabolism (E72.4)
Sibling codes
E72Other disorders of amino-acid metabolismE72.0Disorders of amino-acid transportE72.1Disorders of sulfur-bearing amino-acid metabolismE72.3Disorders of lysine and hydroxylysine metabolismE72.4Disorders of ornithine metabolismE72.5Disorders of glycine metabolismE72.8Other specified disorders of amino-acid metabolismE72.9Disorder of amino-acid metabolism, unspecified