D68.2
Hereditary deficiency of other clotting factors
Coding guidance (WHO 2019)
Congenital afibrinogenaemia Deficiency: AC globulin proaccelerin Deficiency of factor: I [fibrinogen] II [prothrombin] V [labile] VII [stable] X [Stuart-Prower] XII [Hageman] XIII [fibrin-stabilizing] Dysfibrinogenaemia (congenital) Hypoproconvertinaemia Owren disease
Sibling codes
D68Other coagulation defectsD68.0Von Willebrand diseaseD68.1Hereditary factor XI deficiencyD68.3Haemorrhagic disorder due to circulating anticoagulantsD68.4Acquired coagulation factor deficiencyD68.5Primary thrombophiliaD68.6Other thrombophiliaD68.8Other specified coagulation defectsD68.9Coagulation defect, unspecified